Protein CPT1B

URN urn:agi-llid:1375
Name CPT1B
Description carnitine palmitoyltransferase 1B (muscle)
Connectivity 36
Notes The protein encoded by this gene, a member of the carnitine/choline acetyltransferase family, is the rate-controlling enzyme of the long-chain fatty acid beta-oxidation pathway in muscle mitochondria. This enzyme is required for the net transport of long-chain fatty acyl-CoAs from the cytoplasm into the mitochondria. At least four transcript variants encoding two different isoforms have been found for this gene, and one of the transcripts is bicistronic. In addition, two of the transcripts utilize alternative polyadenylation signals.

Swiss-Prot Accession Q92523
Q53FV7
Q924X2
Q3UIM5
Q8CJE9
Q924X3
O70253
Q63704
Q9QWZ9
Q9Z2G4
Q9Z2G5

Unigene ID Hs.439777
Mm.358582
Rn.6028
Hs.654827

KEGG ID hsa:1375
mmu:12895
rno:25756

EC Number 2.3.1.21

Swiss-Prot ID CPT1B_HUMAN
CPT1B_MOUSE
A5PLL0_HUMAN
B7Z4U4_HUMAN
B7Z5T8_HUMAN
Q53FV7_HUMAN
O70253_RAT

Cell Localization Mitochondria

GO ID 0008415
0004095
0005515
0016740
0006853
0006635
0006631
0006629
0046320
0006810
0016021
0016020
0005792
0005741
0005739
0016301
0015909
0019867

Pathway PPARG Brief
Figure 3 CAR 2009
PPARG Targets
New Pathway
PPARalpha Pathway

IPI ID IPI00877658
IPI00640400
IPI00869084
IPI00021925
IPI00878289
IPI00878461
IPI00879031
IPI00136563
IPI00555092
IPI00196647
IPI00209856
IPI00569962

Ariadne Ontology Fatty acid oxidation

Mouse chromosome position 15 52.6 cM

GO Molecular Function protein binding
transferase activity
acyltransferase activity
carnitine O-palmitoyltransferase activity
kinase activity

Homologene ID 22548

Hugo ID 2329

GO Cellular Component membrane
microsome
mitochondrion
mitochondrial outer membrane
integral to membrane

MGI ID 1098297

Human chromosome position 22q13.33

GO Biological Process regulation of fatty acid oxidation
carnitine shuttle
fatty acid beta-oxidation
fatty acid metabolic process
transport
long-chain fatty acid transport
lipid metabolic process

Rat chromosome position 7q34

GenBank ID NC_000022
NM_152245
NP_689451
NM_004377
NP_004368
NM_152246
NP_689452
NT_011526
NW_001838756
NW_927650
NG_003100
AC_000065
AC_000154
NM_001145134
NM_001145135
NM_001145136
NM_001145137
NM_152247
AB003286
BAA21492
CH471138
EAW73568
EAW73569
EAW73570
EAW73571
EAW73572
U62317
AAB03343
AB051457
BAB33340
AI142100
AK223174
BAD96894
AK291316
BAF84005
AK297866
BAH12680
AK299395
BAH13024
BC021130
BC131570
AAI31571
BC142954
AAI42955
BG426428
BI560870
BU615917
CR619413
D87812
BAA13461
DC373481
U62733
AAC51122
U66828
AAB40651
Y08682
CAA69938
Y08683
CAA69939
Q53FV7
Q92523
BC143071
AAI43072
BC150318
AAI50319
NC_000081
NM_009948
NP_034078
NT_039621
NW_001030577
AC_000037
AB085661
BAC24126
AC137513
AJ278284
CAC40149
CAC40150
CH466550
EDL04340
AB010826
BAA88685
AF017174
AAC31640
AK029141
AK146851
BAE27481
BC018270
AAH18270
CJ092541
CJ238532
Q3UIM5
Q8CJE9
Q924X2
Q924X3
NC_005106
NM_013200
NP_037332
NW_001084860
NW_047783
AC_000075
AF029875
AAC40081
AF063302
AAC72744
AAC72745
AAC72746
CH474027
EDL76569
EDL76570
BC085761
AAH85761
D43623
BAA07733
O70253
Q63704
Q9QWZ9
Q9Z2G4
Q9Z2G5
CR600292

Group Fatty acid oxidation
membrane
microsome
mitochondrion
mitochondrial outer membrane
integral to membrane
protein binding
transferase activity
acyltransferase activity
carnitine O-palmitoyltransferase activity
kinase activity
regulation of fatty acid oxidation
carnitine shuttle
fatty acid beta-oxidation
fatty acid metabolic process
transport
long-chain fatty acid transport
lipid metabolic process

RGD ID 2397

LocusLink ID 1375
12895
25756

Alias CPT1-M
M-CPT1
MCCPT1
FLJ55729
FLJ58750
KIAA1670
carnitine palmitoyltransferase 1B
CPTI, muscle
carnitine palmitoyltransferase 1A (muscle)
carnitine O-palmitoyltransferase I, mitochondrial muscle isoform
Cpt1
M-CPTI
carnitine palmitoyltransferase 1b, muscle
M-CPT I
choline/ethanolaminekinase
carnitine palmitoyltransferase 1, muscle
muscle type carnitine palmitoyltransferase I
muscle-type carnitine palmitoyltransferase I
CPT-IB
MGC93637
CPT-Ibeta 1
CPT-Ibeta 3
carnitine palmitoyltransferase Ibeta 1
carnitine palmitoyltransferase Ibeta 2
carnitine palmitoyltransferase Ibeta 3
Carnitine palmitoyltransferase 1 beta, muscle isoform
CPTI-M
muscle carnitine palmitoyltransferase I
carnitine palmitoyltransferase 1B isoform a
carnitine palmitoyltransferase 1B isoform b
Carnitine palmitoyltransferase I like protein
carnitine palmitoyltransferase I, muscle
carnitine palmitoyltransferase 1B (muscle)
CPT1B
mitochondrial Carnitine O-palmitoyltransferase I muscle isoform
carnitine palmitoyltransferase ibeta III
CPT1-Ms
carnitine palmitoyltransferase 1 beta muscle isoform
cpt-ibeta III
cpt-ibeta I
carnitine palmitoyltransferase ibeta I
carnitine palmitoyltransferase 1 beta
LOC129264
LOC150414
M-CPT1s
M-CPT Is

Organism Homo sapiens
Mus musculus
Rattus norvegicus

OMIM ID 601987